Phenylketonuria (PKU) is a disorder where an amino acid called phenylalanine accumulates inappropriately in the body. Phenylalanine is a protein building block the body obtains through the ...

Phenylalanine is metabolized to produce maleylacetoacetate ... leading to the production of black urine.

Blood levels of phe were measured hourly and the aromatic acid metabolites of phe and phenylethylamine (PEA) were estimated in the urine. During the chronic intake blood phe and urine metabolites ...